Dyke-Davidoff-Masson Syndrome: A Case Report in a Filipino Male Adolescent

A previously well young Filipino boy presented with prolonged recurrent left focal to bilateral seizure. He was born of a non-consanguineous marriage, home-delivered vaginally, full term no perinatal complications. had normal growth and developmental milestones until at the age 7 months when he developed febrile status epilepticus. Since then, residual hemiplegia, dysarthria, cognitive delay seizures occurring twice daily. poorly compliant on multiple anti-seizure medications. able go school do activities daily living minimal supervision from his family. Symptoms refractory seizures, hemiparesis, facial asymmetry, intellectual disabilities along brain imaging evidence cerebral hemi-atrophy compensatory calvarial thickening subsequent hyperpneumatization is consistent Dyke-Davidoff-Masson Syndrome (DDMS). rare clinico-neuroradiologic condition in fetal or early childhood period as consequence chronic insult. Diagnosis established clinically characteristic cranial finding. Hemi-spherectomy treatment choice. This case will enlighten our mind aid us prompt recognition this uncommon syndrome classic clinico-radiologic presentation. Multidisciplinary intervention essential, primarily optimize seizure control provide quality life.